Abstract: The clinical manifestations of hemichorea associated with nonketotic hyperglycemia tend  to be diverse.Two cases of  hemichorea  associated  with nonketotic hyperglycemia were admitted  to the hospital.  Case 1 was a recurrent case,  the first presentation was focal dystonia of  the left foot with nonchoreographic movements,  and the second clinical symptom was clearly inconsistent with the imaging changes. In case 2,  there was a unilateral dancelike movement,  and MRI showed bilateral  T1  hypersignaling  lesions.This rare clinical manifestation is helpful for clinicians to further understand the disease and reduce misdiagnosis.

Key words: chorea； nonketosis; , hyperglycemia