Abstract: Kawasaki disease is a systemic vasculitis.  The most serious complications are coronary artery dilatation and coronary artery aneurysm.  The main treatments include highdose gamma globulin intravenous drip and oral aspirin.  G6PD deficiency is usually considered a relative contraindication of aspirin intake.  In this paper,  we reported that the color Doppler ultrasound of children with Kawasaki disease complicated with G6PD deficiency showed coronary aneurysm formation.  After highdose gamma globulin intravenous drip,  plus lowdose aspirin for preventing platelet aggregation,  a successful diagnosis and treatment process was obtained.  And the relevant literature was reviewed to arouse the attention of clinicians and to provide reference for clinical work.

Key words: mucocutaneous lymph node syndrome, glucosephosphate dehydrogenase deficiency, aspirin, anemia, , hemolytic, child