Treatment experience of giant renal hamartoma rupture and hemorrhage in a patient with tuberous sclerosis complex and literature review

doi:10.3969/j.issn.1004-583X.2024.12.009

Abstract

Abstract:

Objective To explore the causes and effective treatment of giant hamartomas. Methods The diagnosis and treatment of 1 case of nodular sclerosis with giant renal angiomyolipoma rupture and hemorrhage were retrospectively analyzed, and the relevant literatures at home and abroad were reviewed. Results The patient was treated with arterial embolization due to rupture and bleeding. After surgery, the patient developed fever and acute kidney injury, with a high risk of rebleeding that requires a renal resection. Conclusion Tuberous sclerosis combined with renal hamartoma is not likely to cause abnormal renal function. For patients with rupture and bleeding, conservative or interventional embolization is preferred. The disease is hereditary in families, and early diagnosis and monitoring are essential.

Key words: tuberous sclerosis, renal hamartoma rupture, interventional embolization

CLC Number:

R742.89

Jia Minnan, Liu Qiong, Xu Ruoyun, Niu Kai. Treatment experience of giant renal hamartoma rupture and hemorrhage in a patient with tuberous sclerosis complex and literature review[J]. Clinical Focus, 2024, 39(12): 1111-1114.

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URL: https://huicui.hebmu.edu.cn/EN/10.3969/j.issn.1004-583X.2024.12.009

https://huicui.hebmu.edu.cn/EN/Y2024/V39/I12/1111

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