Abstract: Interstitial lung disease (ILD) is now increasingly recognized as a frequent and serious complication associated with connective tissue disease (CTD)， and severely influences the life quality of patients. There are substantial differences in the clinical presentations， pathological types and imaging appearances of ILD in each specific CTD. Diagnosis and treatment timely is crucial for the prognosis of patients. The research progress of CTDILD in rencent years was updated in this artical.

Key words: lung diseases, interstitial; , connective tissue disease