原发性干燥综合征并发肺栓塞1例并文献复习

doi:10.3969/j.issn.1004-583X.2021.04.015

摘要/Abstract

摘要：

回顾性分析延安大学附属医院收治1例原发性干燥综合征(Primary Sjögren’s syndrome,pSS)并发肺栓塞患者的病例,并进行相关文献复习。在临床工作中遇到干燥综合征(Sjögren’s syndrome,SS)累及呼吸系统或有活动性炎症的患者要提高警惕,熟记SS肺部表现的鉴别诊断,对于存在多个危险因素或有肺栓塞高风险的患者应及早行CT血管造影(CT angiography, CTA)检查,血栓的形成可能与肺部感染导致的过度炎症反应以及原发病的炎症活动有关。

关键词: 干燥综合征, 肺栓塞, 血栓

Abstract:

This study analyzed the data of a patient with primary Sjögren's syndrome (pSS)complicated with pulmonary embolism admitted to the Yanan University Affiliated Hospital, and reviewed the relevant literature.If SS Patients, who were also related to the respiratory system or active inflammation, are encountered in clinical, they should be vigilant and memorize the differential diagnosis of SS pulmonary manifestations. CT angiography(CTA) should be performed as soon as possible for patients with multiple risk factors or high risk of pulmonary embolism. Thrombosis might be caused by pulmonary infection or inflammatory activity of primary disease.

Key words: Sjögren’s syndrome, pulmonary embolism, thrombus

中图分类号:

R777.2

崔璐, 李静, 刘宇宏. 原发性干燥综合征并发肺栓塞1例并文献复习[J]. 临床荟萃, 2021, 36(4): 361-364.

Cui Lu, Li Jing, Liu Yuhong. Primary Sjögren’s syndrome with pulmonary embolism:a case report and literature review[J]. Clinical Focus, 2021, 36(4): 361-364.

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链接本文: https://huicui.hebmu.edu.cn/CN/10.3969/j.issn.1004-583X.2021.04.015

https://huicui.hebmu.edu.cn/CN/Y2021/V36/I4/361

图/表 3

图1 唇腺活检淋巴细胞多灶性浸润,灶性指数为3,纤维组织轻度增生 a.HE×100;b.HE×200

图2 突发肺栓塞时肺部影像左、右肺动脉及左、右下肺动脉分支肺栓塞,并两下肺局部肺梗死;右肺上叶炎性病变

图3 治疗10天后肺部影像肺动脉主干无増宽,右肺下叶肺动脉少量栓子较前减少,右肺上叶及双肺下叶病变对比前片范围减小;右肺上叶炎性病变较前明显减轻

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